Gregory S. Sawicki, MD, MPH, is a pediatric pulmonologist and health services researcher with particular interest in addressing health outcomes, disease self-management, and adherence for children, adolescents, and young adults with chronic respiratory diseases including cystic fibrosis (CF) and asthma.
Dr. Sawicki’s primary research activities are currently focused on the process and outcomes of transition from pediatric to adult focused health care for adolescents with chronic medical conditions. He is conducting a NIH-funded mixed methods qualitative and survey study of adolescents and young adults with CF with the aim of exploring their current experiences with health care transition and disease self-management. In his recent work, he has helped to develop and validate a survey instrument to assess transition readiness for youth with chronic disease, the Transition Readiness Assessment Questionnaire (TRAQ). This instrument is currently being used in multiple health care transition studies throughout the country. He also is working on the development of quality measures to evaluate the transition to adult care for youth with chronic conditions.
Active Projects
2011-2016 Cystic Fibrosis as a Model for Health Care Transition for Chronically Ill Youth
NHLBI K23 HL105541-01A1
Principal Investigator
The goals of this mentored career development award are to understand the barriers and facilitators of the health care transition process from the perspective of adolescents and young adults with cystic fibrosis. The research will provide important information that can be used in designing health care transition programs for adolescents and young adults with chronic medical conditions.
Research Background
Dr. Sawicki received his MD from Harvard Medical School in 2001. He completed residency in Boston Combined Residency Program in Pediatrics in 2004, followed by fellowship in Pediatric Pulmonology at Boston Children’s Hospital (2004-2007). He also completed the Harvard Pediatric Health Services Research Fellowship in 2007, receiving an MPH in Clinical Effectiveness at the Harvard School of Public Health. Dr. Sawicki is currently the Associate Director of the Cystic Fibrosis Center at Boston Children’s Hospital.
Education
Undergraduate School
Biochemical Sciences
Harvard College
1997
Cambridge
MA
Medical School
Harvard Medical School
2001
Cambridge
MA
Internship
Pediatrics
Boston Children's Hospital
2002
Boston
MA
Residency
Pediatrics Boston Combined Residency Program (BCRP)
Boston
MA
Fellowship
Pediatric Pulmonology Boston Children's Hospital
2007
Boston
MA
Graduate School
Harvard School of Public Health
2007
Boston
MA
Publications
Electromyography-Informed Estimates of Joint Contact Forces Within the Lower Back and Knee Joints During a Diverse Set of Industry-Relevant Manual Lifting Tasks. J Appl Biomech. 2025 Jan 13; 1-10. View Abstract
"It's Like You're Feeding Your Child Twice": Barriers and Facilitators to Human Milk Feeding Children With Cystic Fibrosis. Pediatr Pulmonol. 2025 Jan; 60(1):e27497. View Abstract
Center of mass states render multijoint torques throughout standing balance recovery. J Neurophysiol. 2025 Jan 01; 133(1):206-221. View Abstract
What does it mean to be "healthy" when taking elexacaftor/tezacaftor/ivacaftor (ETI)? A qualitative study. J Cyst Fibros. 2025 Jan; 24(1):187-192. View Abstract
Qualitative understanding of experiences of people with cystic fibrosis in a treatment discontinuation trial: The QUEST study. Contemp Clin Trials. 2025 Jan; 148:107752. View Abstract
Reduced Achilles tendon stiffness in aging associates with higher metabolic cost of walking. J Appl Physiol (1985). 2024 Dec 01; 137(6):1541-1548. View Abstract
Plasma Microbial Cell-Free DNA Metagenomic Next-Generation Sequencing in People With Cystic Fibrosis. Pediatr Pulmonol. 2025 Jan; 60(1):e27380. View Abstract
Impact of Discontinuing Both Hypertonic Saline and Dornase Alfa after Elexacaftor-Tezacaftor-Ivacaftor in Cystic Fibrosis. Ann Am Thorac Soc. 2024 Nov; 21(11):1507-1515. View Abstract
Factors associated with prescription of elexacaftor/tezacaftor/ivacaftor among people with cystic fibrosis aged 12 years or older with at least one F508del allele. J Cyst Fibros. 2025 Jan; 24(1):135-141. View Abstract
Safety and tolerability of a low glycemic load dietary intervention in adults with cystic fibrosis: a pilot study. Front Nutr. 2024; 11:1441201. View Abstract
Self-reported chronic therapy use after 24-weeks of follow-up by participants who completed the simplify randomized, controlled trial. J Cyst Fibros. 2025 Jan; 24(1):91-97. View Abstract
Overview and Updates in Pediatric Pulmonary Medicine. Clin Chest Med. 2024 Sep; 45(3):xiii-xiv. View Abstract
Center of mass states render multi-joint torques throughout standing balance recovery. bioRxiv. 2024 Aug 19. View Abstract
Development and preliminary validation of the personalized cystic fibrosis medication questionnaire (PCF-MQ). J Cyst Fibros. 2024 Nov; 23(6):1100-1105. View Abstract
Cross-Cutting mHealth Behavior Change Techniques to Support Treatment Adherence and Self-Management of Complex Medical Conditions: Systematic Review. JMIR Mhealth Uhealth. 2024 May 01; 12:e49024. View Abstract
Advances in Care and Outcomes for Children with Cystic Fibrosis. Clin Chest Med. 2024 Sep; 45(3):625-637. View Abstract
The effects of plantarflexor weakness and reduced tendon stiffness with aging on gait stability. PLoS One. 2024; 19(4):e0302021. View Abstract
A Data-Driven Approach to Estimate Human Center of Mass State During Perturbed Locomotion Using Simulated Wearable Sensors. Ann Biomed Eng. 2024 Aug; 52(8):2013-2023. View Abstract
An emotional journey: caregiver experiences with gastrostomy tube decision-making for children with cystic fibrosis. J Cyst Fibros. 2024 Sep; 23(5):1000-1006. View Abstract
Continuous glucose monitoring and advanced glycation endproducts for prediction of clinical outcomes and development of cystic fibrosis-related diabetes in adults with CF. Front Endocrinol (Lausanne). 2024; 15:1293709. View Abstract
Habitually wearing high heels may improve user walking economy in any footwear. J Appl Physiol (1985). 2024 Mar 01; 136(3):567-572. View Abstract
Safety and Pharmacokinetics Following Oral or Intravenous Lefamulin in Adults With Cystic Fibrosis. Clin Ther. 2024 02; 46(2):96-103. View Abstract
Randomized Trial of the Insulin-Only iLet Bionic Pancreas for the Treatment of Cystic Fibrosis- Related Diabetes. Diabetes Care. 2024 Jan 01; 47(1):101-108. View Abstract
Reduced Achilles tendon stiffness in aging persists at matched activations and associates with higher metabolic cost of walking. bioRxiv. 2023 Nov 27. View Abstract
Clinician perspectives and practices related to sexual and reproductive care provision for males with cystic fibrosis. J Cyst Fibros. 2024 May; 23(3):417-423. View Abstract
Simulations suggest walking with reduced propulsive force would not mitigate the energetic consequences of lower tendon stiffness. PLoS One. 2023; 18(10):e0293331. View Abstract
Attenuation of muscle spindle firing with artificially increased series compliance during stretch of relaxed muscle. Exp Physiol. 2024 01; 109(1):148-158. View Abstract
Predictive Control of Peak Achilles Tendon Force in a Simulated System of the Human Ankle Joint with a Parallel Artificial Actuator During Hopping. IEEE Int Conf Rehabil Robot. 2023 09; 2023:1-6. View Abstract
American Society of Biomechanics Journal of Biomechanics Award 2021: Exploring the Functional Boundaries and Metabolic Consequences of Triceps Surae Force-Length Relations during Walking. J Biomech. 2023 09; 158:111771. View Abstract
Attenuation of muscle spindle firing with artificially increased series compliance during stretch of relaxed muscle. bioRxiv. 2023 May 09. View Abstract
Partners in research: The success with therapies research consortium and the CF community unite to improve self-management. J Cyst Fibros. 2023 09; 22(5):830-835. View Abstract
The influence of induced gait asymmetry on joint reaction forces. J Biomech. 2023 05; 153:111581. View Abstract
Perturbing the muscle work loop paradigm to unravel the neuromechanics of unsteady locomotion. J Exp Biol. 2023 04 01; 226(7). View Abstract
High deductible insurance plans impart economic burden for people with cystic fibrosis. Pediatr Pulmonol. 2023 06; 58(6):1798-1801. View Abstract
How many billions is enough? Prioritizing profits over patients with cystic fibrosis. Pediatr Pulmonol. 2023 05; 58(5):1595-1597. View Abstract
Long-term tezacaftor/ivacaftor safety and efficacy in people with cystic fibrosis and an F508del-CFTR mutation: 96-week, open-label extension of the EXTEND trial. J Cyst Fibros. 2023 May; 22(3):464-470. View Abstract
EFFECT OF ELEXACAFTOR/TEZACAFTOR/IVACAFTOR ON ANNUAL RATE OF LUNG FUNCTION DECLINE IN PEOPLE WITH CYSTIC FIBROSIS. J Cyst Fibros. 2023 May; 22(3):402-406. View Abstract
Clinician perspectives on assessing for disordered eating and body image disturbance in adolescents and young adults with cystic fibrosis. J Cyst Fibros. 2023 May; 22(3):431-435. View Abstract
Discontinuation versus continuation of hypertonic saline or dornase alfa in modulator treated people with cystic fibrosis (SIMPLIFY): results from two parallel, multicentre, open-label, randomised, controlled, non-inferiority trials. Lancet Respir Med. 2023 04; 11(4):329-340. View Abstract
Rate of Lung Function Decline in People with Cystic Fibrosis Having a Residual Function Gene Mutation. Pulm Ther. 2022 Dec; 8(4):385-395. View Abstract
Sexual and reproductive health experiences and care of adult women with cystic fibrosis. J Cyst Fibros. 2023 03; 22(2):223-233. View Abstract
Real-world feasibility of short-term, unsupervised home spirometry in CF. Pediatr Pulmonol. 2022 12; 57(12):3129-3135. View Abstract
Eating disorders in adolescents and young adults with cystic fibrosis. Pediatr Pulmonol. 2022 11; 57(11):2791-2797. View Abstract
Author Reply to: Empowering Without Misinforming Adolescents and Young Adults with Cystic Fibrosis. Comment on "Perceptions of Social Media Use to Augment Health Care Among Adolescents and Young Adults With Cystic Fibrosis: Survey Study". JMIR Pediatr Parent. 2022 May 25; 5(2):e39450. View Abstract
Continuous Glucose Monitoring and HbA1c in Cystic Fibrosis: Clinical Correlations and Implications for CFRD Diagnosis. J Clin Endocrinol Metab. 2022 03 24; 107(4):e1444-e1454. View Abstract
Understanding the Intersection between Gender Transition and Health Outcomes in Cystic Fibrosis. Ann Am Thorac Soc. 2022 03; 19(3):504-506. View Abstract
A Phase 3, open-label, 96-week trial to study the safety, tolerability, and efficacy of tezacaftor/ivacaftor in children = 6 years of age homozygous for F508del or heterozygous for F508del and a residual function CFTR variant. J Cyst Fibros. 2022 07; 21(4):675-683. View Abstract
Men's sexual and reproductive health in cystic fibrosis in the era of highly effective modulator therapies-A qualitative study. J Cyst Fibros. 2022 07; 21(4):657-661. View Abstract
Engaging Stakeholders in the Development of a Reproductive Goals Decision AID for Women with Cystic Fibrosis. J Patient Exp. 2022; 9:23743735221077527. View Abstract
The Relationship between Body Composition, Dietary Intake, Physical Activity, and Pulmonary Status in Adolescents and Adults with Cystic Fibrosis. Nutrients. 2022 Jan 12; 14(2). View Abstract
Exploring provider attitudes and perspectives related to men's health in cystic fibrosis. J Cyst Fibros. 2022 07; 21(4):652-656. View Abstract
Trajectories of the Transition Readiness Assessment Questionnaire Among Youth With Inflammatory Bowel Disease. J Clin Gastroenterol. 2022 10 01; 56(9):805-809. View Abstract
Financial impacts of the COVID-19 pandemic on cystic fibrosis care: lessons for the future. J Cyst Fibros. 2021 12; 20 Suppl 3:16-20. View Abstract
Patient and family experience of telehealth care delivery as part of the CF chronic care model early in the COVID-19 pandemic. J Cyst Fibros. 2021 12; 20 Suppl 3:41-46. View Abstract
Remote monitoring in telehealth care delivery across the U.S. cystic fibrosis care network. J Cyst Fibros. 2021 12; 20 Suppl 3:57-63. View Abstract
Evaluating barriers to and promoters of telehealth during the COVID-19 pandemic at U.S. cystic fibrosis programs. J Cyst Fibros. 2021 12; 20 Suppl 3:9-13. View Abstract
Prevalence, variability, and predictors of sinus surgery in pediatric patients with cystic fibrosis. Pediatr Pulmonol. 2021 12; 56(12):4029-4038. View Abstract
The effect of elexacaftor/tezacaftor/ivacaftor (ETI) on glycemia in adults with cystic fibrosis. J Cyst Fibros. 2022 03; 21(2):258-263. View Abstract
Favorable Clinician Acceptability of Telehealth as Part of the Cystic Fibrosis Care Model during the COVID-19 Pandemic. Ann Am Thorac Soc. 2021 09; 18(9):1588-1592. View Abstract
Perceptions of Social Media Use to Augment Health Care Among Adolescents and Young Adults With Cystic Fibrosis: Survey Study. JMIR Pediatr Parent. 2021 Aug 16; 4(3):e25014. View Abstract
Evaluating the Impact of Stopping Chronic Therapies after Modulator Drug Therapy in Cystic Fibrosis: The SIMPLIFY Clinical Trial Study Design. Ann Am Thorac Soc. 2021 08; 18(8):1397-1405. View Abstract
Disease burden in people with cystic fibrosis heterozygous for F508del and a minimal function mutation. J Cyst Fibros. 2022 01; 21(1):96-103. View Abstract
The Effects of Ivacaftor on Bone Density and Microarchitecture in Children and Adults with Cystic Fibrosis. J Clin Endocrinol Metab. 2021 03 08; 106(3):e1248-e1261. View Abstract
Ivacaftor in Infants Aged 4 to <12 Months with Cystic Fibrosis and a Gating Mutation. Results of a Two-Part Phase 3 Clinical Trial. Am J Respir Crit Care Med. 2021 03 01; 203(5):585-593. View Abstract
Rapid Implementation of Telehealth Services in a Pediatric Pulmonary Clinic During COVID-19. Pediatrics. 2021 07; 148(1). View Abstract
An evaluation of healthcare utilization and clinical charges in children and adults with cystic fibrosis. Pediatr Pulmonol. 2021 05; 56(5):928-938. View Abstract
Long-term safety and efficacy of tezacaftor-ivacaftor in individuals with cystic fibrosis aged 12 years or older who are homozygous or heterozygous for Phe508del CFTR (EXTEND): an open-label extension study. Lancet Respir Med. 2021 07; 9(7):733-746. View Abstract
Improvement of Pulmonary Function in Cystic Fibrosis Patients following Endoscopic Sinus Surgery. Laryngoscope. 2021 09; 131(9):1930-1938. View Abstract
Tribulations and (clinical) trials in cystic fibrosis. J Cyst Fibros. 2021 03; 20(2):188-190. View Abstract
Transition Readiness Not Associated With Measures of Health in Youth With IBD. Inflamm Bowel Dis. 2021 01 01; 27(1):49-57. View Abstract
Men's health in the modern era of cystic fibrosis. J Cyst Fibros. 2021 11; 20(6):e121-e123. View Abstract
Monogenic Diabetes in a Child with Cystic Fibrosis: A Case Report and Review of the Literature. J Endocr Soc. 2021 Jan 01; 5(1):bvaa165. View Abstract
Decreased survival in cystic fibrosis patients with a positive screen for depression. J Cyst Fibros. 2021 01; 20(1):120-126. View Abstract
Survey of patients with cystic fibrosis and caregivers decisions regarding CFTR modulators. Pediatr Pulmonol. 2020 11; 55(11):2983-2989. View Abstract
Caregiver Burden Due to Pulmonary Exacerbations in Patients with Cystic Fibrosis. J Pediatr. 2019 12; 215:164-171.e2. View Abstract
Male gender and unemployment are associated with lower levels of perceived social support in adults with cystic fibrosis. J Psychosom Res. 2019 12; 127:109858. View Abstract
Medical Deferred Action - Living on Borrowed Time. N Engl J Med. 2019 Oct 24; 381(17):1601-1603. View Abstract
Predictors of pulmonary exacerbation treatment in cystic fibrosis. J Cyst Fibros. 2020 05; 19(3):407-414. View Abstract
A phase 3 study of tezacaftor in combination with ivacaftor in children aged 6 through 11?years with cystic fibrosis. J Cyst Fibros. 2019 09; 18(5):708-713. View Abstract
Disease progression in patients with cystic fibrosis treated with ivacaftor: Data from national US and UK registries. J Cyst Fibros. 2020 01; 19(1):68-79. View Abstract
Chronic rhino-sinusitis treatment in children with cystic fibrosis: A cross-sectional survey of pediatric pulmonologists and otolaryngologists. Int J Pediatr Otorhinolaryngol. 2019 Sep; 124:139-142. View Abstract
An open-label extension study of ivacaftor in children with CF and a CFTR gating mutation initiating treatment at age 2-5?years (KLIMB). J Cyst Fibros. 2019 11; 18(6):838-843. View Abstract
Developing Sexual and Reproductive Health Educational Resources for Young Women with Cystic Fibrosis: A Structured Approach to Stakeholder Engagement. Patient. 2019 04; 12(2):267-276. View Abstract
Linkage of the CF foundation patient registry with the pediatric health information system database. Pediatr Pulmonol. 2019 06; 54(6):721-728. View Abstract
Interprofessional provider educational needs and preferences regarding the provision of sexual and reproductive health care in cystic fibrosis. J Cyst Fibros. 2019 09; 18(5):671-676. View Abstract
Social support is associated with fewer reported symptoms and decreased treatment burden in adults with cystic fibrosis. J Cyst Fibros. 2019 07; 18(4):572-576. View Abstract
Cystic Fibrosis And Ivacaftor Use: The Authors Reply. Health Aff (Millwood). 2019 02; 38(2):328. View Abstract
Safety, pharmacokinetics, and pharmacodynamics of lumacaftor and ivacaftor combination therapy in children aged 2-5 years with cystic fibrosis homozygous for F508del-CFTR: an open-label phase 3 study. Lancet Respir Med. 2019 04; 7(4):325-335. View Abstract
Healthcare expenditures for privately insured US patients with cystic fibrosis, 2010-2016. Pediatr Pulmonol. 2018 12; 53(12):1611-1618. View Abstract
Disparities in Mortality of Hispanic Patients with Cystic Fibrosis in the United States. A National and Regional Cohort Study. Am J Respir Crit Care Med. 2018 10 15; 198(8):1055-1063. View Abstract
Transition to adulthood and adult health care for patients with sickle cell disease or cystic fibrosis: Current practices and research priorities. J Clin Transl Sci. 2018 Oct; 2(5):334-342. View Abstract
Rate and predictors of prescription of lumacaftor - Ivacaftor in the 18?months following approval in the United States. J Cyst Fibros. 2018 11; 17(6):742-746. View Abstract
Sexual and Reproductive Health of Young Women With Cystic Fibrosis: A Concept Mapping Study. Acad Pediatr. 2019 04; 19(3):307-314. View Abstract
The burden of cystic fibrosis in the Medicaid population. Clinicoecon Outcomes Res. 2018; 10:423-431. View Abstract
Data from the US and UK cystic fibrosis registries support disease modification by CFTR modulation with ivacaftor. Thorax. 2018 08; 73(8):731-740. View Abstract
Precision Medicine In Action: The Impact Of Ivacaftor On Cystic Fibrosis-Related Hospitalizations. Health Aff (Millwood). 2018 05; 37(5):773-779. View Abstract
Perspectives of adolescent girls with cystic fibrosis and parents on disease-specific sexual and reproductive health education. Pediatr Pulmonol. 2018 08; 53(8):1027-1034. View Abstract
Association of High-Dose Ibuprofen Use, Lung Function Decline, and Long-Term Survival in Children with Cystic Fibrosis. Ann Am Thorac Soc. 2018 04; 15(4):485-493. View Abstract
Cystic fibrosis patient registries: A valuable source for clinical research. J Cyst Fibros. 2018 07; 17(4):433-440. View Abstract
Outcome evaluation of a pharmacy-based therapy management program for patients with cystic fibrosis. Pediatr Pulmonol. 2018 06; 53(6):720-727. View Abstract
Risk Factors for Gaps in Care during Transfer from Pediatric to Adult Cystic Fibrosis Programs in the United States. Ann Am Thorac Soc. 2018 02; 15(2):234-240. View Abstract
Ceftaroline pharmacokinetics and pharmacodynamics in patients with cystic fibrosis. J Cyst Fibros. 2018 05; 17(3):e25-e31. View Abstract
Lung function decline is delayed but not decreased in patients with cystic fibrosis and the R117H gene mutation. J Cyst Fibros. 2018 07; 17(4):503-510. View Abstract
Sexual and reproductive health care utilization and preferences reported by young women with cystic fibrosis. J Cyst Fibros. 2018 01; 17(1):64-70. View Abstract
Mental Health Screening of Medically-Admitted Patients With Cystic Fibrosis. Psychosomatics. 2018 Mar - Apr; 59(2):158-168. View Abstract
Incident Stenotrophomonas maltophilia infection and lung function decline in cystic fibrosis. Pediatr Pulmonol. 2017 10; 52(10):1276-1282. View Abstract
Early Lung Function Decline in Cystic Fibrosis. Can Registry Data Explain Divergent Phenotypes? Am J Respir Crit Care Med. 2017 08 15; 196(4):407-409. View Abstract
Pediatric lung transplantation and end of life care in cystic fibrosis: Barriers and successful strategies. Pediatr Pulmonol. 2017 Nov; 52(S48):S61-S68. View Abstract
Sexual and reproductive health behaviors and experiences reported by young women with cystic fibrosis. J Cyst Fibros. 2018 01; 17(1):57-63. View Abstract
Preparation for Transition to Adult Care Among Medicaid-Insured Adolescents. Pediatrics. 2017 Jul; 140(1). View Abstract
Patients with Cystic Fibrosis and a G551D or Homozygous F508del Mutation: Similar Lung Function Decline. Am J Respir Crit Care Med. 2017 06 15; 195(12):1673-1676. View Abstract
Impact of an Individual Mandate and Other Health Reforms on Dependent Coverage for Adolescents and Young Adults. Health Serv Res. 2018 06; 53(3):1581-1599. View Abstract
Utilization of a patient-centered asthma passport tool in a subspecialty clinic. J Asthma. 2018 02; 55(2):180-187. View Abstract
Microbiology of the Upper and Lower Airways in Pediatric Cystic Fibrosis Patients. Otolaryngol Head Neck Surg. 2017 08; 157(2):302-308. View Abstract
Correlation of Transient Elastography With Severity of Cystic Fibrosis-related Liver Disease. J Pediatr Gastroenterol Nutr. 2017 04; 64(4):505-511. View Abstract
The CF-CARES primary palliative care model: A CF-specific structured assessment of symptoms, distress, and coping. J Cyst Fibros. 2018 01; 17(1):71-77. View Abstract
Adherence and Recursive Perception Among Young Adults with Cystic Fibrosis. Anthropol Med. 2017 Apr; 24(1):65-80. View Abstract
Counterpoint: Too little care or too little collaboration: Approaches to treatment refusal in CF. J Cyst Fibros. 2017 03; 16(2):304-305. View Abstract
Provider Attitudes and Practices toward Sexual and Reproductive Health Care for Young Women with Cystic Fibrosis. J Pediatr Adolesc Gynecol. 2017 Oct; 30(5):546-552. View Abstract
Reply: Combining Clinical Trial and Patient Registry Data in Cystic Fibrosis: Who Should Be Compared? Am J Respir Crit Care Med. 2017 02 01; 195(3):405-406. View Abstract
Obesity and Airway Dysanapsis in Children with and without Asthma. Am J Respir Crit Care Med. 2017 Feb 01; 195(3):314-323. View Abstract
Assessment of safety and efficacy of long-term treatment with combination lumacaftor and ivacaftor therapy in patients with cystic fibrosis homozygous for the F508del-CFTR mutation (PROGRESS): a phase 3, extension study. Lancet Respir Med. 2017 02; 5(2):107-118. View Abstract
Treatment satisfaction in cystic fibrosis: early patient experience with tobramycin inhalation powder. Patient Prefer Adherence. 2016; 10:2163-2169. View Abstract
Strategies to optimize treatment adherence in adolescent patients with cystic fibrosis. Adolesc Health Med Ther. 2016; 7:117-124. View Abstract
Transition and transfer of childhood cancer survivors to adult care: A national survey of pediatric oncologists. Pediatr Blood Cancer. 2017 02; 64(2):346-352. View Abstract
Healthcare resource utilization associated with ivacaftor use in patients with cystic fibrosis. J Med Econ. 2016 Sep; 19(9):845-51. View Abstract
Young adults with cystic fibrosis have altered trabecular microstructure by ITS-based morphological analysis. Osteoporos Int. 2016 08; 27(8):2497-505. View Abstract
Safety, pharmacokinetics, and pharmacodynamics of ivacaftor in patients aged 2-5 years with cystic fibrosis and a CFTR gating mutation (KIWI): an open-label, single-arm study. Lancet Respir Med. 2016 Feb; 4(2):107-15. View Abstract
Risk Factors for Hearing Loss in Patients with Cystic Fibrosis. J Am Acad Audiol. 2016 01; 27(1):6-12. View Abstract
Tackling the increasing complexity of CF care. Pediatr Pulmonol. 2015 Oct; 50 Suppl 40:S74-9. View Abstract
Sustained Benefit from ivacaftor demonstrated by combining clinical trial and cystic fibrosis patient registry data. Am J Respir Crit Care Med. 2015 Oct 01; 192(7):836-42. View Abstract
Early Life Growth Trajectories in Cystic Fibrosis are Associated with Pulmonary Function at Age 6 Years. J Pediatr. 2015 Nov; 167(5):1081-8.e1. View Abstract
Development and Validation of the Adolescent Assessment of Preparation for Transition: A Novel Patient Experience Measure. J Adolesc Health. 2015 Sep; 57(3):282-7. View Abstract
Rate of Uptake of Ivacaftor Use after U.S. Food and Drug Administration Approval among Patients Enrolled in the U.S. Cystic Fibrosis Foundation Patient Registry. Ann Am Thorac Soc. 2015 Aug; 12(8):1146-52. View Abstract
A randomized controlled trial of vitamin D replacement strategies in pediatric CF patients. J Cyst Fibros. 2016 Mar; 15(2):234-41. View Abstract
Self-Management and Transition Readiness Assessment: Concurrent, Predictive and Discriminant Validation of the STARx Questionnaire. J Pediatr Nurs. 2015 Sep-Oct; 30(5):668-76. View Abstract
Predictors of timing of transfer from pediatric- to adult-focused primary care. JAMA Pediatr. 2015 Jun; 169(6):e150951. View Abstract
Similar performance of Brasfield and Wisconsin scoring systems in young children with cystic fibrosis. Pediatr Radiol. 2015 Oct; 45(11):1624-8. View Abstract
Randomized trial of efficacy and safety of dornase alfa delivered by eRapid nebulizer in cystic fibrosis patients. J Cyst Fibros. 2015 Nov; 14(6):777-83. View Abstract
Development and evaluation of a palliative care curriculum for cystic fibrosis healthcare providers. J Cyst Fibros. 2016 Jan; 15(1):90-5. View Abstract
Antibiotic treatment of signs and symptoms of pulmonary exacerbations: a comparison by care site. Pediatr Pulmonol. 2015 May; 50(5):431-40. View Abstract
Ready, set, stop: mismatch between self-care beliefs, transition readiness skills, and transition planning among adolescents, young adults, and parents. Clin Pediatr (Phila). 2014 Oct; 53(11):1062-8. View Abstract
The Transition Readiness Assessment Questionnaire (TRAQ): its factor structure, reliability, and validity. Acad Pediatr. 2014 Jul-Aug; 14(4):415-22. View Abstract
Compromised bone microarchitecture and estimated bone strength in young adults with cystic fibrosis. J Clin Endocrinol Metab. 2014 Sep; 99(9):3399-407. View Abstract
Inter-hospital variation in the frequency of sinus surgery in children with cystic fibrosis. Pediatr Pulmonol. 2015 Mar; 50(3):231-235. View Abstract
Motivating adherence among adolescents with cystic fibrosis: youth and parent perspectives. Pediatr Pulmonol. 2015 Feb; 50(2):127-36. View Abstract
Transition care: future directions in education, health policy, and outcomes research. Acad Pediatr. 2014 Mar-Apr; 14(2):120-7. View Abstract
Vitamin D status in children with cystic fibrosis. Associations with inflammation and bacterial colonization. Ann Am Thorac Soc. 2014 Feb; 11(2):205-10. View Abstract
Transition and transfer of adolescents and young adults with pediatric onset chronic disease: the patient and parent perspective. J Pediatr Rehabil Med. 2014; 7(1):43-51. View Abstract
Brasfield and Wisconsin scoring systems have equal value as outcome assessment tools of cystic fibrosis lung disease. Pediatr Radiol. 2014 May; 44(5):529-34. View Abstract
Longitudinal trends in health-related quality of life in adults with cystic fibrosis. Chest. 2013 Sep; 144(3):981-989. View Abstract
Claim-based analyses of inhaled corticosteroid refill rates for asthma: who's kidding whom? Ann Am Thorac Soc. 2013 Apr; 10(2):149-50. View Abstract
Treatment complexity in cystic fibrosis: trends over time and associations with site-specific outcomes. J Cyst Fibros. 2013 Sep; 12(5):461-7. View Abstract
A pulmonary exacerbation risk score among cystic fibrosis patients not receiving recommended care. Pediatr Pulmonol. 2013 Oct; 48(10):954-61. View Abstract
Referral patterns and perceived barriers to adult congenital heart disease care: results of a survey of U.S. pediatric cardiologists. J Am Coll Cardiol. 2012 Dec 11; 60(23):2411-8. View Abstract
Managing treatment complexity in cystic fibrosis: challenges and opportunities. Pediatr Pulmonol. 2012 Jun; 47(6):523-33. View Abstract
Erratum to: Psychometric evaluation of the Cystic Fibrosis Questionnaire-Revised in a national, US sample. Qual Life Res. 2012 Sep; 21(7):1279-90. View Abstract
The impact of reflux burden on Pseudomonas positivity in children with cystic fibrosis. Pediatr Pulmonol. 2012 Jun; 47(6):582-7. View Abstract
Psychometric evaluation of the Cystic Fibrosis Questionnaire-Revised in a national sample. Qual Life Res. 2012 Sep; 21(7):1267-78. View Abstract
Physician practices for communicating with patients with cystic fibrosis about the use of noninvasive and invasive mechanical ventilation. Chest. 2012 Apr; 141(4):1010-1017. View Abstract
Assessment of current strategies for weaning premature infants from supplemental oxygen in the outpatient setting. Adv Neonatal Care. 2011 Oct; 11(5):349-56. View Abstract
Receipt of health care transition counseling in the national survey of adult transition and health. Pediatrics. 2011 Sep; 128(3):e521-9. View Abstract
Reduced mortality in cystic fibrosis patients treated with tobramycin inhalation solution. Pediatr Pulmonol. 2012 Jan; 47(1):44-52. View Abstract
Tree nut allergy, egg allergy, and asthma in children. Clin Pediatr (Phila). 2011 Feb; 50(2):133-9. View Abstract
Longitudinal assessment of health-related quality of life in an observational cohort of patients with cystic fibrosis. Pediatr Pulmonol. 2011 Jan; 46(1):36-44. View Abstract
Employment experiences among adolescents and young adults with cystic fibrosis. Disabil Rehabil. 2011; 33(11):922-6. View Abstract
Associations between illness perceptions and health-related quality of life in adults with cystic fibrosis. J Psychosom Res. 2011 Feb; 70(2):161-7. View Abstract
Uncontrolled asthma in a commercially insured population from 2002 to 2007: trends, predictors, and costs. J Asthma. 2010 Jun; 47(5):574-80. View Abstract
Cystic fibrosis and transition to adult medical care. Pediatrics. 2010 Mar; 125(3):566-73. View Abstract
Asthma care quality for children with minority-serving providers. Arch Pediatr Adolesc Med. 2010 Jan; 164(1):38-45. View Abstract
Patterns of inhaled corticosteroid use and asthma control in the Childhood Asthma Management Program Continuation Study. Ann Allergy Asthma Immunol. 2010 Jan; 104(1):30-5. View Abstract
Measuring the transition readiness of youth with special healthcare needs: validation of the TRAQ--Transition Readiness Assessment Questionnaire. J Pediatr Psychol. 2011 Mar; 36(2):160-71. View Abstract
Travel patterns to school among children with asthma. Clin Pediatr (Phila). 2009 Jul; 48(6):632-40. View Abstract
The impact of MRSA on lung function in patients with cystic fibrosis. Am J Respir Crit Care Med. 2009 Apr 15; 179(8):734-5; author reply 735. View Abstract
The impact of incident methicillin resistant Staphylococcus aureus detection on pulmonary function in cystic fibrosis. Pediatr Pulmonol. 2008 Nov; 43(11):1117-1123. View Abstract
High treatment burden in adults with cystic fibrosis: challenges to disease self-management. J Cyst Fibros. 2009 Mar; 8(2):91-6. View Abstract
Advance care planning in adults with cystic fibrosis. J Palliat Med. 2008 Oct; 11(8):1135-41. View Abstract
Necrotising pneumonia is an increasingly detected complication of pneumonia in children. Eur Respir J. 2008 Jun; 31(6):1285-91. View Abstract
Self-reported physical and psychological symptom burden in adults with cystic fibrosis. J Pain Symptom Manage. 2008 Apr; 35(4):372-80. View Abstract
Periodic use of inhaled steroids in children with mild persistent asthma: what are pediatricians recommending? Clin Pediatr (Phila). 2008 Jun; 47(5):446-51. View Abstract
Bronchoscopy findings in children and young adults with tracheostomy due to congenital anomalies and neurological impairment. J Pediatr Rehabil Med. 2008; 1(2):137-43. View Abstract
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Self-reported involvement of family members in the care of adults with CF. J Cyst Fibros. 2008 Mar; 7(2):95-101. View Abstract
Adults with cystic fibrosis report important and unmet needs for disease information. J Cyst Fibros. 2007 Nov 30; 6(6):411-6. View Abstract
Phenotypic and cytokine analysis of human peripheral blood gamma delta T cells expressing NK cell receptors. J Immunol. 1997 Oct 15; 159(8):3723-30. View Abstract